Bentall Procedure for an Adolescent with Sickle Cell Disease, Hodgkin’s Lymphoma, and old Cerebrovascular Accident
Cardiopulmonary bypass (CPB) in patients with sickle cell anemia can trigger lethal vaso-occlusive crises, especially in cases of hypoxia, hypothermia, acidosis, or low-ﬂow states. We described a patient with sickle cell anemia who had bicuspid aortic valve stenosis and aneurysmal dilatation of the ascending aorta complicated with infective endocarditis. The patient had a history of stroke. During routine workup, Hodgkin’s Lymphoma was diagnosed. The patient underwent exchange transfusion preoperatively and immediately before the initiation of CPB. We performed a Bentall procedure, and the patient was discharged in a stable condition. Sickle Cell Disease can be very challenging during CPB, and special precautions are required to prevent vaso-occlusive crises.