Bentall Procedure for an Adolescent with Sickle Cell Disease, Hodgkin’s Lymphoma, and old Cerebrovascular Accident

Ahmed Elmahrouky; Hani Barnawi; Hassan  Alshehri; Majed  Almutairi; Ghadeer  Mokhtar; Ahmed  Jamjoom; Uthman Al Uthman

doi:10.35810/ects.v3i1.165

Ahmed Elmahrouky 1. Division of Cardiac Surgery, Cardiovascular Department, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia 2. Cardiothoracic Surgery Department, Tanta University, Tanta, Egypt.
Hani Barnawi Faculty of Medicine, King Saud Bin Abdulaziz University for Health Science, Jedda, Saudi Arabia
Hassan Alshehri Department of Cardiothoracic Surgery, Perfusion Services, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia
Majed Almutairi Department of Cardiothoracic Surgery, Perfusion Services, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia
Ghadeer Mokhtar Department of pathology, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia
Ahmed Jamjoom Division of Cardiac Surgery, Cardiovascular Department, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia
Uthman Al Uthman Division of Cardiac Surgery, Cardiovascular Department, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia

DOI: https://doi.org/10.35810/ects.v3i1.165

Keywords: Sickle Cell Disease, Hodgkin’s Lymphoma, Aortic valve replacement, Cardiopulmonary bypass, Aortic root replacement, Vaso-occlusive crisis

Abstract

Cardiopulmonary bypass (CPB) in patients with sickle cell anemia can trigger lethal vaso-occlusive crises, especially in cases of hypoxia, hypothermia, acidosis, or low-ﬂow states. We described a patient with sickle cell anemia who had bicuspid aortic valve stenosis and aneurysmal dilatation of the ascending aorta complicated with infective endocarditis. The patient had a history of stroke. During routine workup, Hodgkin’s Lymphoma was diagnosed. The patient underwent exchange transfusion preoperatively and immediately before the initiation of CPB. We performed a Bentall procedure, and the patient was discharged in a stable condition. Sickle Cell Disease can be very challenging during CPB, and special precautions are required to prevent vaso-occlusive crises.